Hemophagocytic lymphohystiocytosis (HLH) represents a severe hyper-inflammatory condition with the cardinal symptoms prolonged fever, hepatosplenomegaly, and cytopenias. The most prominent histopatho-logical feature of HLH is an accumulation of activated T lymphocytes and macrophages predominantly in lymphoid tissues. Although it can occur in all age groups, neonatal-onset HLH is very rare. The present study reported a case of HLH presenting with anemia and hepatosplenomegally at age of two month.
 

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